Votre recherche pour: 2-(Methylamino)isobutyric+acid+hydrate

127 842 les résultats ont été trouvés

Affiner les résultats Trier par

Sort Results

Vue liste Vue simple

Comparer(0) Effacer

Évaluez le résultat de cette recherche

Isobutyrate d'isobutyle 98,0 GC_ASSAY_METHOD

Fournisseur: TCI

Description: Isobutyrate d'isobutyle 98,0 GC_ASSAY_METHOD

Anti-ETFA Rabbit Polyclonal Antibody

Numéro de catalogue: (PRSI26-842)

Fournisseur: ProSci Inc.

Description: ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids.ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene.

UOM: 1 * 50 µG

Promotion